Congenital Anomaly of the Intrahepatic Portal System Complicated by Intrahepatic Cholangiocellular Carcinoma -A Case Report-

Atsushi Kimura, Kenichi Takayasu, Tatsuya Yamada, Masatoshi Makuuchi*, Susumu Yamazaki*, Hiroshi Hasegawa*

Department of Diagnostic Radiology, National Cancer Center Hospital
*Department of Surgery, National Cancer Center Hospital

Recent progress in diagnostic imaging such as ultrasonography, computed tomography and percutaneus transhepatic portography, allows better comprehension of the anatomy of the intrahepatic portal and venous systems. We report here a patient with an abnormal intrahepatic portal system; cul-de-sac-like dilatation of the right anterior portal vein coming off from the left portal vein, agenesis of the umbilical portion of the left portal vein and the development of a right hepatic round ligament. This entity most likely originates in abnormal development of the fetus. It is indispensable for hepatectomy to understand the intrahepatic portal system as seen in diagnostic modalities.

Key words
right hepatic round ligament, congenital anomaly of the intrahepatic portal system, dynamic CT

Reprint requests
Atsushi Kimura Department of Diagnostic Radiology, National Cancer Center Hospital
5-1-1 Tukiji, Chuoh-ku, Tokyo, 104 JAPAN

Accepted
November 8, 1989

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