A Case of Malignant Solid-Pseudopapillary Tumor of the Pancreas Associated with Dorsal Agenesis

Hideki Ijichi, Takahiro Terashi, Takeshi Shiraishi, Ikuo Takahashi, Hiroya Wada, Takashi Nishizaki, Yuichi Kobayashi¹⁾, Kouji Joko¹⁾, Shigetoshi Murata²⁾ and Yumi Oshiro³⁾

Department of Surgery, Department of Center for Liver and Biliary Diseases¹⁾, Department of Radiology²⁾ and Department of Pathology³⁾, Matsuyama Red Cross Hospital

A 62-year-old woman seen for a cystic tumor of the pancreas was found in abdominal computed tomography (CT) to have an absence of the dorsal pancreas and the presence of a 9 cm cystic tumor in the head of the pancreas. PET/CT for tumor FDG uptake indicated high malignant potential, although intraoperative cytological diagnosis by fine-needle aspiration was benign. Because malignancy could not be completely ruled out by frozen section diagnosis of solid components, we conducted pancreatic resection with lymph node dissection. Subsequent pathological examination showed a solid-pseudopapillary tumor (SPT) with vascular and lymphatic invasion. Reports of malignant SPT of the pancreas associated with dorsal agenesis are extremely rare, and we discuss the relevant literature.

Key words
solid-pseudopapillary tumor, pancreas, dorsal agenesis

Reprint requests
Hideki Ijichi Department of Surgery, Matsuyama Red Cross Hospital
1 Bunkyomachi, Matsuyama, 790-8524 JAPAN

Accepted
October 22, 2008

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