A Case of Primary Retroperitoneal Cystadenocarcinoma with Difficulty of Preoperative Diagnosis

Junya Morimoto, Kiyosi Maeda, Eiji Noda, Toru Inoue, Nobuya Yamada, Tetuji Sawada, Masaichi Oohira, Yukio Nishiguchi*, Teruyuki Ikehara* and Kousei Hirakawa

Department of Surgical Oncology, Osaka City University Graduate School Division of Medicine
Department of Surgery, Osaka City General Medical Center*

Primary retroperitoneal cystadenocarcinoma is a very rare tumor. A 56-year-old woman who was diagnosed as having a retroperitoneal tumor presented to our hospital with lower abdominal pain and bloody stool. Radical surgery was carried out and the macroscopic findings showed that the tumor was 11×13 cm in diameter and oval in shape with smooth surface, and the lumen with multiple elevated portion was occupied with mucous fluid and a muddy brown substance. Pathological studies showed some atypical papillary cells and a vestigial of Mullerian system. Also both ovaries were normal-sized. Thus, the definitive diagnosis was primary retroperitoneal cystadenocarcinoma with direct invasion to the rectum and vagina, and multiple lymph nodes metastases. After undergoing adjuvant chemotherapy with low dose CDDP/TS-1, the woman is still alive without recurrence 1 year 2 months after the operation.

Key words
retroperitoneal tumor, cystadenocarcinoma

Reprint requests
Junya Morimoto Department of Surgical Oncology, Osaka City University Graduate School Division of Medicine
1-4-3 Asahimachi, Abeno-ku, Osaka, 545-8585 JAPAN

Accepted
December 16, 2009

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