A Case of Duodenal Leiomyoblastoma Accompanied with von Recklinghausen's Disease

Takao Hinoi, Hisashi Ohshiro, Yasuji Yamamoto, Issei Tanaka, Kazuo Inagaki, Naoki Haruta, Hideki Ohdan, Masafumi Kikkawa, Tamaki Nakatani, Kazuaki Miyamoto

The First Department of Surgery, Hiroshima Prefectal Hiroshima Hospital

Duodenal leiomyoblastoma is an exceedingly rare disease and 14 cases including ours have been reported in Japan. This is the first case of the leiomyoblastoma combined with von Recklinghausen's disease. The patient was a 56-year-old man who had a past history and family history of von Recklinghausen's disease. He was admitted with the complaint of a right hypochondrial tumor. Under the diagnosis of a smooth muscle tumor located in the 1st portion of the duodenum and a gastric ulcer, tumor resection and total gastrectomy (Roux-Y) was performed. The histological diagnosis was leiomyoblastoma and from its size, the evidence of infiltration and pleomorphism it was thought to be malignant though there was no metastasis to regional lymph nodes. Twenty months after the operation the patient is still alive without evidence of recurrence. He should be carefully followed up because the biological behavior of leiomyoblastoma is still controversial.

Key words
duodenal leiomyoblastoma, Recklinghausen's disease

Reprint requests
Takao Hinoi The First Department of Surgery, Hiroshima Prefectual Hiroshima Hospital
1-1-54 Ujinakanda, Minami-ku, Hiroshima-shi, 734 JAPAN

Accepted
October 7, 1992

To read the PDF file you will need Abobe Reader installed on your computer.