A Case of Gastric Leiomyoblastoma in a Child

Yoshinari Hashimoto, Hiroshi Fukuda, Syoji Matsui, Tsutomu Fujimoto, Tomoaki Urakawa*

Department of Surgery, Kakogawa Municipal Hospital
*Department of Surgery, Kobe Rosai Hospital of Labour Welfare Corporation

We report a case of gastric leiomyoblastoma in a child. An ll-year-old boy was admitted because of vomiting and melena. Laboratory data showed severe anemia (RBC 184×10⁴/mm³, Hb 5.2 g/dl, Ht 16.6%) and hypoproteinemia (4.7 g/dl). Upper gastrointestinal series and gastroendoscopy showed a sub-mucosal tumor with central erosion in the anterior wall of the stomach body, about 3 cm in diameter. Distal partial gastrectomy combined with dissection of perigastric lymph nodes was performed. The resected specimen showed a submucosal tumor on the stomach body, measuring 4×2.5×1.7 cm in size, with a central ulcer. Histological examination revealed leiomyoblastoma of the stomach (atypical oval cells each with a clear space near the nucleus), and no metastasis to lymph nodes. The postoperative course was uneventful. Ultrasonography of the abdomen showed no remarkable findings, and gallium scintigraphy showed no hot lesion in the chest or abdomen. We finally diagnosed Ieiomyoblastoma of stomach in a child. Four cases of gastric leiomyoblastoma in childhood have been reported in Japan, with 13 cases (11 female) in the world literature. Seven cases had Carney's triad: gastric leiomyoblastoma, functioning extraadenal paraganglioma and lung chondroma. Our case did not have this triad. In following the clinical course of children with gastric leiomyoblastoma, special attention must be paid to the possibility of Carney's triad.

Key words
gastric leiomyoblastoma in childhood, Carney's triad

Reprint requests
Yoshinari Hashimoto Department of Surgery, Kakogawa Municipal Hospital
135 Morita, Okubo-cho, Akashi-shi, 674 JAPAN

Accepted
September 8, 1993

To read the PDF file you will need Abobe Reader installed on your computer.