A Case Report of Lymphangiomyomatosis in the Mesenterium

Nobuo Takenouchi, Tetsuya Miura, Setsuyuki Ootake, Takafumi Kusaka, Masaru Fujimori, Yoshiaki Sekishita, Tsuneo Shiono, Shinjuro Kuroshima, Jun Yamaguchi¹⁾

Department of Surgery, Department of Pathology¹⁾, Obihiro Kosei Hospital

We present a rare case of lymphangiomyomatosis of the mesenterium. A 28-year-old woman was referred to our hospital with the chief complaint of left side abdominal pain. CT scan revealed a giant mass in the mesenterium from the renal level to the pelvic space. At laparotomy, the tumor was localized in the mesenterium, but invaded to the jejunum. The tumor was completely excised with jejunum resection. The resected specimen included a cystic tumor and was 3 kg in weight. Histological examination of the tumor revealed lyphangiomyomatosis. Lymphangiomyomatosis is a very rare disease that occurs predominantly in women of reproductive age, mainly in the mediastinum, lung and retroperitoneal space. Only four other cases of lymphangiomyomatosis arising from the mesenterium have been reported in the world literature.

Key words
lymphangiomyomatosis, mesenterium

Reprint requests
Nobuo Takenouchi Department of Surgery, Obhiro Kosei Hospital
Nishi 6 Minami 8, Obihiro, 080 JAPAN

Accepted
November 1, 1993

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