Presacral Schwannoma in a Patient with von Recklinghausen's Disease: Case Report

Masato Watanabe, Nami Ishikawa, Nobuhisa Kameoka, Naoyuki Matoba, Terumasa Fujii, Hiroshi Masuda, Kazuhiro Satoh and Takako Iwata^*

Department of Surgery, Yamaguchi Red Cross Hospital and Faculty of Health Sciences, Yamaguchi University School of Medicine^*

A 53-year-old woman admitted with presacral tumor confused initially with ovarian cystoma was diagnosed with von Recklinghausen's disease based on physical findings, and an elastic hard mass was palpable on the posterior wall of the rectum. CT scan and MRI showed a solid cystic tumor 7 cm in diameter in the presacral space. Angiography showed a hypervascular mass fed by the middle and left lateral sacral arteries. We suspected the tumor was a malignant peripheral nerve sheath tumor, and extirpated it. The specimen was a 8× 6× 5 cm yellowish solid cystic tumor weighing 130g. The histopathological diagnosis was schwannoma. Presacral schwannoma in a patient with von Recklinghausen's disease is quite rare, and has not, to our knowledge, been reported in the literature except for 1 case.

Key words
neurofibromatosis 1, presacral tumor, schwannoma

Reprint requests
Masato Watanabe Department of Surgery, Yamaguchi Red Cross Hospital, 53-1 Yahatababa, Yamaguchi, 753-8519 JAPAN

Accepted
January 30, 2002

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