A Case of Malignant Schwannoma of the Jejunum with Liver Metastasis and Peritoneal Dissemination

Kazuhito Yajima, Mutsuo Yamamoto, Norio Katayanagi, Hideki Saithou and Osamu Aizawa

Department of Surgery, Niigata City General Hospital

We report a case of malignant schwannoma of the jejunum not associated with von Recklinghausen's disease. A 61-year-old man seen for epigastralgia was found in computed tomography (CT) to have an irregularly enhanced tumor in the lower abdominal cavity and several metastatic liver tumors. Barium examination of the small intestine, abdom inal angiography, and scintigraphy suggested a malignant tumor arising from the small intestine. Laparotomy showed a 10×10cm tumor in the jejunum, with metastatic liver tumors of the segments No. 5, 6, and 8 and peritoneal dissemination. We partially resected the jejunum, and conducted right hepatic lobectomy, and resected of the peritoneal disseminated tumors. Immunohistochemical S-100 protein staining was positive, so pathologic examination indicated malignant schwannoma of the jejunum. Malignant schwannoma of the small intestine not associated with Von Recklinghausen's disease is extremely rare and only 13 cases have, to our knowledge, been reported in Japan. This is also first case of long-term survival, at 2 years 9 months, without recurrence after hepatectomy and resection of peritoneal dissemination.

Key words
malignant schwannoma, small intestine, liver metastasis and peritoneal dissemination

Reprint requests
Kazuhito Yajima Department of Surgery, Niigata City General Hospital
2-6-1 Shichikuyama, Niigata-shi, 950-8739 JAPAN

Accepted
February 27, 2002

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