A Case of the Successful Surgical Treatment for Gardner's Syndrome Associated with the Recurrent Giant Desmoid Tumor

Toru Saito, Nobuhiro Takiguchi, Hiroaki Soda, Takehide Asano, Matsuo Nagata, Hiroshi Yamamoto and Kazuo Watanabe

Department of Gastroenterological Surgery, Chiba Cancer Center Hospital

We successfully treated Gardner's syndrome associated with recurrent giant desmoid tumor involving the massive intestine, right ureter, and IVC. A 51-year-old woman suffering from ileus due to a recurrent abdominal tumor and admitted in August 2002 had already undergone proximal gastrectomy, subtotal colectomy, and resection of abdominal tumors three times. First, we tried conservative treatment, because we considered the risk of difficult surgery, postoperative short bowel syndrome, and lowered quality of life. Despite conservative therapy, emergency surgery was required due to hypovolemic shock caused by melena. After the tumor was extirpated, the length of remnant small intestine was about 100 cm. In postoperative nutrition, she consumed gruel and home intravenous hyperalimentation for three months postoperatively, because of short bowel syndrome. Given nutritional status and diarrhea control, she stopped hyperalimentation and began normal eating with antidiarrheic drugs every day four months after operation. Now she is free from the disease and maintains a high quality of life.

Key words
Gardner's syndrome, desmoid tumor, short bowel syndrome

Reprint requests
Toru Saito Department of General Surgery, Graduate School of Medicine, Chiba University
1-8-1 Inohana, Chuo-ku, Chiba, 260-8670 JAPAN

Accepted
March 30, 2005

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